Herlyn Werner Wünderlich Syndrome. Presentation of Case and Review of Literature
DOI:
https://doi.org/10.53903/01212095.128Keywords:
Multidetector computed tomography, Magnetic resonance imaging, Mullerian ducts, Female urogenital diseasesAbstract
Herlyn Werner Wünderlich Syndrome is a rare and undiagnosed mullerian malformation, characterized by the triad of clogged hemivagina, ipsilateral renal agenesis and didelphic uterus; its diagnosis is usually late due to the unspecific symptomatology it produces: abdominal pain, dysmenorrhea and palpable abdominal mass secondary to hematocolpos, causing serious changes in fertility. The use of diagnostic images such as ultrasound, tomography and magnetic resonance imaging is essential to diagnose this type of anomaly. The case of a 12-year-old patient with this condition and a review of the literature are presented.
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