Peutz-Jeghers syndrome associated with intestinal obstruction due to intususception, a rare disease with a frequent complication. Case report
DOI:
https://doi.org/10.53903/01212095.263Keywords:
Tomografia computarizada, Neoplasias abdominales, Intususcepción, Sindrome Peutz JeghersAbstract
Peutz-Jeghers syndrome, is an autosomal dominant neoplastic syndrome characterized by the formation of hamartomatous polyps along the gastrointestinal tract, typical mucocutaneous pigmentations, and an elevated lifetime risk of cancer. We present the case of a 21-year-old woman with a known history of Peutz-Jeghers syndrome, without follow-up, who presents symptoms of abdominal pain, nausea and emesis with intolerance to oral intake, with a tomographic study and upper Gi series that lead to the diagnosis of small bowel obstruction with intussusception at the level of the second portion of the duodenum. This article reviews the literature and the radiological features of Peutz-Jeghers syndrome.
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