Heterotaxy syndrome associated with Polysplenia (left isomerism). About a case

Authors

  • Cesar Augusto Zabaleta Arias Clínica Belo Horizonte, Neiva
  • Carlos Emilio Polo Rivera Clínica Belo Horizonte, Neiva
  • Jimer Orlando Parra Hernández Clínica Belo Horizonte, Neiva

DOI:

https://doi.org/10.53903/01212095.266

Keywords:

Heterotaxy syndrome, Ambiguus, situs, Dyspnea

Abstract

The heterotaxy syndrome associated with polysplenia (left isomerism) is part of what is known as Heterotaxia or Ambiguous Situs where a random location of the thoraco-abdominal organs is observed with or without vital functional compromise. We present a case of an 80-year-old male patient, with a history of high blood pressure, type 2 diabetes mellitus, who was admitted for dyspnea, weakness and abdominal pain. During his stay he progresses to multiple organ failure and dies. Among the rigorous studies, chest and abdominal tomography allows evidence of a series of anatomical alterations.

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References

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Published

2023-09-30

How to Cite

(1)
Zabaleta Arias, C. A.; Polo Rivera, C. E.; Parra Hernández, J. O. Heterotaxy Syndrome Associated With Polysplenia (left isomerism). About a Case. Rev. colomb. radiol. 2023, 34, 6020-6025.

Issue

Vol. 34 No. 3 (2023): Julio - Septiembre

Section

Case reports

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