Sickle cell anemia in images from head-to-toe
DOI:
https://doi.org/10.53903/01212095.320Keywords:
Anemia, sickle cell, Diagnostic imaging, Radiology, v, PediatricsAbstract
Sickle cell disease (SCD) is an autosomal recessive entity characterized by abnormal hemoglobin formation. The manifestations of SCD are mainly due to vaso-occlusive crises, hemolysis or infection and usually present with multisystem involvement. For the most part, clinical and imaging findings will suggest the diagnosis and allow adequate follow-up. Different diagnostic modalities such as ultrasound, computed tomography and magnetic resonance imaging play an essential role in identifying complications of SCD. Knowledge of the different specific radiological manifestations of the disease will allow us to make a correct differential diagnosis with other hematologic diseases, an adequate follow-up of this pathology and an early and timely treatment. With this article we intend to familiarize the radiologist with the SCD multisystemic spectrum in the pediatric population.
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